Hexacosanoic acid

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Hexacosanoic acid
2D structure for Hexacosanoic acid
Chemical Name hexacosanoic acid
Chemical Formula C26H52O2
CAS Number 506-46-7
Chemical Information HMDB02356
Biochemical Taxonomy

  • Fatty Acids

Functional Taxonomy Not Available
Nutritional Taxonomy Not Available
Metabolic Pathways Not Available
Biofluid Location

  • Blood

Tissue Location

  • Fibroblasts
  • Adrenal Gland

Normal Biofluid Concentrations

  • Blood: 0.83 +/- 0.45 umol/L

Normal Tissue Concentrations Not Available
Diseases / Conditions Related to Nutrition

  • Patients with adrenomyeloneuropathy

Other (Monogenic Disorders)

Abnormal Biofluid Concentrations

  • Blood (Patients with adrenomyeloneuropathy): 2.42 +/- 6.43 umol/L

Abnormal Tissue Concentrations Not Available
Physiological Processes Not Available
Authors:
Affiliations:

Contents

Introduction

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X-linked adrenoleukodystrophy (X-ALD) is a peroxisomal disorder biochemically characterized by the accumulation of very long chain fatty acids (VLCFA), particularly hexacosanoic acid (C(26:0)) and tetracosanoic acid (C(24:0)), in tissues and biological fluids. (PMID 16750542)

Biological Function

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Catabolism

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Diseases / Conditions Related to Nutrition

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  • Patients with adrenomyeloneuropathy

Other (Monogenic) Disorders

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Nutritional Information

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Drivers for biological variation

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Vulnerable groups

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Other resources

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Links

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