Aminoadipic acid

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Aminoadipic acid
2D structure for Aminoadipic acid
Chemical Name	2-aminohexanedioic acid
Chemical Formula	C₆H₁₁NO₄
CAS Number	542-32-5
Chemical Information	HMDB00510
Biochemical Taxonomy	Amino Acids
Functional Taxonomy	Not Available
Nutritional Taxonomy	Not Available
Metabolic Pathways	Alanine and Aspartate Metabolism Arginine and D-Ornithine Metabolism Glutathione Metabolism Glycine, Serine and Threonine Metabolism Pantothenate and CoA Biosynthesis Valine, Leucine and Isoleucine Biosynthesis Valine, Leucine and Isoleucine Degradation
Biofluid Location	Blood
Tissue Location	Not Available
Normal Biofluid Concentrations	Blood: 2.0 (0.0-5.0) umol/L
Normal Tissue Concentrations	Not Available
Diseases / Conditions Related to Nutrition	Patients with alpha-aminoadipic aciduria
Other (Monogenic Disorders)	Kearns-sayre syndrome OMIM: 530000
Abnormal Biofluid Concentrations	Blood (Patients with alpha-aminoadipic aciduria): 6.0 (7.0-8.0) umol/L
Abnormal Tissue Concentrations	Not Available
Physiological Processes	Not Available

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Introduction

guidelines
A metabolite in the principal biochemical pathway of lysine. It antagonizes neuroexcitatory activity modulated by the glutamate receptor, N-methyl-D-aspartate; (NMDA). Alpha-aminoadipate is an intermediate in the metabolism of lysine and saccharopine.(Wikipedia)