3-Methyl-2-oxovaleric acid

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3-Methyl-2-oxovaleric acid
2D structure for 3-Methyl-2-oxovaleric acid
Chemical Name (3S)-3-methyl-2-oxo-pentanoic acid
Chemical Formula C6H10O3
CAS Number 1460-34-0
Chemical Information HMDB00491
Biochemical Taxonomy

  • Keto-Acids

Functional Taxonomy

  • Essential Amino Acid

Nutritional Taxonomy Not Available
Metabolic Pathways

  • Valine, Leucine and Isoleucine Degradation

Biofluid Location

  • Blood
  • Cerebrospinal Fluid (CSF)

Tissue Location Not Available
Normal Biofluid Concentrations

  • Blood: 18.0 (8.0-31.0) uM
  • Blood: 22.7 +/- 4.6 uM
  • Cerebrospinal Fluid (CSF): 2.0 +/- 2.0 uM

Normal Tissue Concentrations Not Available
Diseases / Conditions Related to Nutrition Not Available
Other (Monogenic Disorders) Not Available
Abnormal Biofluid Concentrations Not Available
Abnormal Tissue Concentrations Not Available
Physiological Processes Not Available
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Contents

Introduction

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Biological Source: Metabolite of isoleucine in man, animals and bacteria Metabolism: Precursor to isoleucine in plants Biological Use/Importance: Clinical marker for maple syrup urine disease (ChemNetBase)

Biological Function

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Catabolism

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Diseases / Conditions Related to Nutrition

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Other (Monogenic) Disorders

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Nutritional Information

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Drivers for biological variation

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Vulnerable groups

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Other resources

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Links

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