From NuGOwiki
The NuGOwiki Metabolite Database is a joint initiative of NuGO and HMDB
| Taxonomy Navigation Box; search by |
|
All Metabolites | Biochemical | Nutritional | Functional | Metabolic Pathways | Diseases | Phenotypes | Physiological Processes | Protein |
| Butyrylcarnitine | |
|---|---|
 | |
| Chemical Name | 3-butanoyloxy-4-trimethylammonio-butanoate |
| Chemical Formula | C11H21NO4 |
| CAS Number | 25576-40-3 |
| Chemical Information | HMDB02013 |
| Biochemical Taxonomy |
|
| Functional Taxonomy | Not Available |
| Nutritional Taxonomy | Not Available |
| Metabolic Pathways | Not Available |
| Biofluid Location |
|
| Tissue Location |
|
| Normal Biofluid Concentrations |
|
| Normal Tissue Concentrations | Not Available |
| Diseases / Conditions Related to Nutrition |
|
| Other (Monogenic Disorders) | Not Available |
| Abnormal Biofluid Concentrations |
|
| Abnormal Tissue Concentrations | Not Available |
| Physiological Processes | Not Available |
| Authors: | |
| Affiliations: |
Contents |
Introduction
guidelines
Butyrylcarnitine is elevated in patients with acyl-coa dehydrogenase, short-chain (SCAD) deficiencyin; in infants with acute acidosis and generalized muscle weakness; and in middle-aged patients with chronic myopathy localized in muscle. (OMIM 201470)
Biological Function
Catabolism
Diseases / Conditions Related to Nutrition
- Patients with celiac disease
Other (Monogenic) Disorders