Alpha-1 Antitrypsin

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Alpha-1 Antitrypsin
[[Image:{{{Image}}}|thumb|220px|2D structure for Alpha-1 Antitrypsin]]
Chemical Name
Chemical Formula
CAS Number
Chemical Information
Biochemical Taxonomy
Functional Taxonomy
Nutritional Taxonomy
Metabolic Pathways
Biofluid Location
Tissue Location
Normal Biofluid Concentrations
Normal Tissue Concentrations
Diseases / Conditions Related to Nutrition
Other (Monogenic Disorders)
Abnormal Biofluid Concentrations
Abnormal Tissue Concentrations
Physiological Processes
Authors: L. Pellis
Affiliations: TNO, the Netherlands


Contents

Introduction

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Alpha-1 antitrypsin is a liver protein that blocks the destructive effects of certain enzymes. Alpha-1 antitrypsin deficiency results from a genetic defect. The mechanism that causes associated liver disease and emphysema in some people with this deficiency is not known. However some evidence suggests that it may be related to inflammation. Approximately 75% of adults with severe deficiency will develop emphysema, which often begins before 40 years of age. Smoking can increase risk.

Biological Function

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Alpha-1-antitrypsin is a protease inhibitor.

Catabolism

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Diseases / Conditions Related to Nutrition

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Associated decreased protein/metabolite profile

Associated increased protein/metabolite profile

Other (Monogenic) Disorders

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Nutritional Information

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Drivers for biological variation

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Vulnerable groups

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Other resources

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Links

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OMIM

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