2-Aminoisobutyric acid

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2-Aminoisobutyric acid
2D structure for 2-Aminoisobutyric acid
Chemical Name 2-amino-2-methyl-propanoic acid
Chemical Formula C4H9NO2
CAS Number 62-57-7
Chemical Information HMDB01906
Biochemical Taxonomy

  • Amino Acids

Functional Taxonomy Not Available
Nutritional Taxonomy Not Available
Metabolic Pathways Not Available
Biofluid Location

  • Blood

Tissue Location Not Available
Normal Biofluid Concentrations

  • Blood: 0.75 +/- 0.33 umol/L
  • Blood: 1.03 +/- 0.34 umol/L

Normal Tissue Concentrations Not Available
Diseases / Conditions Related to Nutrition Not Available
Other (Monogenic Disorders) Not Available
Abnormal Biofluid Concentrations Not Available
Abnormal Tissue Concentrations Not Available
Physiological Processes Not Available
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Contents

Introduction

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Aminoisobutyric acid is a nonprotein amino acid (is an end product of pyrimidine metabolism) excreted in the urine of about 5% of healthy individuals (PMID 14806475), and high excretion is an autosomal recessive phenotype (PMID 13058271)

Biological Function

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Catabolism

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Diseases / Conditions Related to Nutrition

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Other (Monogenic) Disorders

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Nutritional Information

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Drivers for biological variation

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Vulnerable groups

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Other resources

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Links

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