2,4-dihydroxybutanoic acid

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2,4-dihydroxybutanoic acid
2D structure for 2,4-dihydroxybutanoic acid
Chemical Name 2,4-dihydroxy-Butanoic acid
Chemical Formula C4H8O4
CAS Number 1518-62-3
Chemical Information HMDB00360
Biochemical Taxonomy

  • Hydroxy Acids

Functional Taxonomy Not Available
Nutritional Taxonomy Not Available
Metabolic Pathways Not Available
Biofluid Location

  • Blood
  • Urine

Tissue Location Not Available
Normal Biofluid Concentrations

  • Blood: 2.0 (0.0-7.0) uM
  • Urine: 4.0 (1.9-15.2) umol/mmol creatinine
  • Urine: 5.0 (2.7-18.7) umol/mmol creatinine
  • Urine: 5.4 (2.5-7.3) umol/mmol creatinine
  • Urine: 7.8 (1.9-18.4) umol/mmol creatinine
  • Urine: 8.1 (4.9-19.3) umol/mmol creatinine

Normal Tissue Concentrations Not Available
Diseases / Conditions Related to Nutrition Not Available
Other (Monogenic Disorders) Not Available
Abnormal Biofluid Concentrations Not Available
Abnormal Tissue Concentrations Not Available
Physiological Processes Not Available
Authors:
Affiliations:

Contents

Introduction

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3-Deoxytetronic acid is usually absent in normal human urine extracts or in only trace constituents in neonates. (PMID 1192581) However, various cases of succinic semialdehyde dehydrogenase deficiency have shown consistently increased amounts of this metabolite. (PMID 3126356)

Biological Function

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Catabolism

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Diseases / Conditions Related to Nutrition

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Other (Monogenic) Disorders

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Nutritional Information

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Drivers for biological variation

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Vulnerable groups

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Other resources

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Links

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